Autoimmune sclerosing

pancreatitisSamreen Raza, MD

PGY-3

Autoimmune pancreatitis

• Numerous names• Sclerosis of the pancreas (Sarles, 1961)• Chronic sclerosing pancreatitis• Lymphoplasmacytic sclerosing pancreatitis• Nonalcoholic duct destructive pancreatitis• Sclerosing pancreatitis• Sclerosing pancreaticocholangitis• Autoimmube chronic pancreatitis

• Autoimmune pancreatitis (Yoshida, 1995)

Autoimmune pancreatitis epidemiology• National survey in Japan (2002)• Prevalence – 0.82/100,000

Clinical presentation

• Acute: • Acute/recurrent episodes of pancreatitis - rare• Painless obstructive jaundice (ddx pancreatic cancer)

• Subacute/late: • Persistent pancreatic mass• Atrophic pancreas +/- calcifications• Unexplained steatorrhea