henosh shnelein purpura

7/30/2019 henosh shnelein purpura

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varies from 6 months toadulthood, peak incidence is 2-8 years.

aredeposited on arterioles, capillaries, and

venules.


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Almost in all cases

Begins as: maculopapular rash petechiae &purpura.

Symmetric, over extensor surfaces & buttocks

Lesions occur in cropsand last 3-10days.


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Occurs in: 80% of cases.

Prominent whichsometimes tender but without erythema andwarmth.

(if present) are serous (nothemorrhagic).

Symptoms are (resolves in a few days)with no permanent damage to the joints.


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Of the 40% of patients who develop kidneyinvolvement, almost all have evidence (visibleor on urinalysis) of blood in the urine. Morethan half also have proteinuria.

but nephrotic syndrome, HTN, acute renal

failure can occur


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Occurs in 62% of cases.

The is colicky in character, and

may be accompanied by.

Complicated by: gastrointestinal hemorrhage,

bowel ischemia and necrosis, intussusceptionand bowel perforation.


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Occurs in 1.3-13.6% of reported series.

The is usually a

are

In contrast to idiopathic intussusception where 80-

90% are .

incases of intussusceptions in HSP as they are oftenconfined to the small bowel


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especially when the child already hasabdominal symptoms & signs.

inview of the underlying intestinal vasculitis &may not be accessible by the enema as it isusually located in the small intestine.


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A -year-old was admitted toour institute with a

history ofon the buttocks

and the extensor aspects of the

forearm and. Urinalysis revealed

microscopic .


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On the next day, she sufferedof ,

tenderness all over theabdomen and.

showed bilious drainage.


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A togetherwith confirmed thediagnosis of intussusceptions.

in view of the patientsclinical condition as well as theunderlying vasculitis.


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At , anwas identified and

reduced manually with somedifficulty.

Though the bowel was congestedlooking and viable, a

was found

and resection with primaryanastomosis was mandatory.


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The post-operative period:

showed till she passed stool and

tolerated oral feeding beforebeen discharged on the 5thpostoperative day.


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henosh shnelein purpura