Fibrous dysplasia: A case report on Treatment of Shapherd crooks deformity in Firous dysplasia -

Embed Size (px)

Citation preview

  • 8/14/2019 Fibrous dysplasia: A case report on Treatment of Shapherd crooks deformity in Firous dysplasia -

    1/7

    ;

    !"#"$$% !'"(#)#(%* +$%,-#. />..$;$ 4>18,9#.7

    :"#2#5=63?0 8$%,- H I(#'K#9>.>;*7

    K aksi riplrt l`-

    Xriktoi`t lg Qbkpbirh arllfs higlroety e`

    Gerlus hyspcksek

    Hr. ^kretlsb Abk`hrk Hid`ktb ;Ksslaekti ^rlg , ,Hr.Fkze Qbkoeouzzkok`4Kssest . ^rlg , Hr.Quder Busske` 1 Kssest . Tijestrkr , Hr. Oh. @kzruc Es cko8Tisehi`t Qurjil` , Hipkrtoi`t lg Lrtbpihea Xrkuoktlcljy.Qbkbiih Qubrkwkrhy Oisheakc Alcciji Blspetkc . Hbkfk-;4>:, Dk`jckhisb .

    QuooiryGedrlus hyspcksek tbi cisel` lg dl`i al`seste`j lg errijuckrcy

    krrk`jih dl`i trkdiaucki e` dck`h gedrlus tessui. Et es tbiaystea cisel` lg dl`i tbkt ak` wikfi` k`h cikh tl pktblcljeakcgrkaturi. Et ak` e`vlcvi k se`jci dl`i (ol`lstktea gedrlushyspcksek), dut e` ltbir et oky e`vlcvis ok`y dl`is(plcylstltea gedrlus hyspcksek). Xbi sivirety lg tbi heslrhirrk`jis grlo eslcktih sokcc cisel` tbkt rioke`s ksyoptlokteatl cisel`s tbkt akusi ripiktih pktblcljeakc grkaturi &higlroety lg tbi dl`i. K ylu`j okci pktei`t kdlut 4> yikrs lch

    akoi tl us wetb buji aystea cisel` e` tbi prlxeokc giour wetb

    pktblcljeakc grkaturi, typeakccy f`lw` ks Qbipbirhs Arllfhiglroety. Xbi ldmiat lg tbes aksi riplrt es tl bejbcejbt tbibuji higlroety wetb pktblcljeakc grkaturi & iopbkses tbisurjeakc prlaihuri wbiri alrriatel` lg tbi dl`y higlroety dylstiltloy, dl`i stri`jtbi`e`j k`h dl`i u`el` dy oexih dl`ijrkgt bks dii` kabeivih sktesgkatlrecy e` k se`jci surjeakcprlaihuri.

  • 8/14/2019 Fibrous dysplasia: A case report on Treatment of Shapherd crooks deformity in Firous dysplasia -

    2/7

    4

    E`trlhuatel`

    Olst kutblrs diceivi gedrlus hyspcksek es k hiviclpoi`tkck`lokcy lg dl`i glroktel` tbkt oky ixest e` k ol`lstktea lr

    plcylstktea glro. E` gedrlus hyspckses trkdiauckr dl`i esripckaih dy aiccuckr gedrlus tessui. Eg tbi cisel`s kri ckrji tbidl`i es al`sehirkdcy wikfi`ih k`h tbi pktblcljeakc grkaturiwetb prljrissevi higlroety oky laaur. Qokcc se`jci cisel`s kriksyoptloktea. Dut pktei`ts wetb plcylstktea hesiksi prisi`t e`abechbllh lr khlcisai`t wetb pke`, ceop, dl`y i`ckrjioi`t,higlroety & pktblcljeakc grkaturi. Gedrlus hyspcksek ak` laaure` tbi ipepbyses, oitkpbysea lr hekpbyses tbkt kggiats tbi reds,tedek, giour, okxecck, sfucc, buoirus, picves, rkheus k`h rkricyspe`i. @uodir lg dl`i e`vlcvioi`t e` plcylstktea gedrlushyspcksek vkreis grlo 4-;4, tbi olst alool` e`vlcvioi`t e`ol`lstktea vkreity es giour. Et kppikrs e` abechbllh k`h okyprljrissevicy i`ckrji. Xbiy kri ciss katevi lr e`katevi e`sficitkc okturety dut rkricy ak` tbiy jrlw e` khuct. Gedrlushyspcksek oky di ksslaektih wetb prialaelus pudirty k`hhkrfcy pejoi`tih sfe` cisel`s akccih Kcdrejbt sy`hrloi. R-Tkylg tbi cisel` sblws rkhel-cuai`t aystea kriks e` tbi oitkpbysealr sbkgt wbeab al`tke`s gedrlus tessui wetb heggusi splts lgeookturi dl`i, tbi cuai`t pktabis typeakccy bkvi k scejbtcy

    bkzy lr jrlu`h jckss kppikrk`ai. Xbi wiejbt dikre`j dl`ioky di`h e` okssevi lstilcytea cisel` k`h l`i lg tbi acksseagikturi es Qbipbirhs arllf higlroety lg prlxeokc giour.Okcej`k`t trk`sglroktel` tl gedrlskralok laaurs e` 9-;>% lgpktei`ts wetb plcylstktea cisel`s dut l`cy rkricy e` ol`lstksteacisel`s.

  • 8/14/2019 Fibrous dysplasia: A case report on Treatment of Shapherd crooks deformity in Firous dysplasia -

    3/7

    1

    Aksi riplrt

    K 4> yikrs lch dly akoi tl us wetb heggeaucty e` wkcfe`j glr :ol`tbs. Bi aluch `lt wkcf wetblut supplrt. Bi bkh k bestlry

    lg oech trkuok tl tbi rejbt tbejb :ol`tbs dkaf Bi `lteaihoech kabe`j pke` e` rejbt uppir tbejb wetb jrkhukc sblrti`e`jk`h di`he`j e` rejbt tbejb. Bes rejbt clwir ceod wkssblrti`ih dy 9 ao. lg bes giolrkc alopl`i`t k`h buji bkrhswicce`j wks sii` e` tbi rejbt uppir tbejb. Kd`lrokc oldecetylg tbi uppir giour wetb olhirkti ti`hir`iss wks glu`h.

    E`vistejktel`s

    ;. R-Tky lg tbi rejbt uppir giour sblws k bujilstilcytea cisel` e`vlcve`j rejbt uppir giour, rejbt

    trlabk`tir, wetb clss lg alrteakc dl`i k`h cuai`tpktabis typeakccy bkzy cllfs cefi jrlw` jcksskppikrk`ai wetb pktblcljeakc grkaturi kt tbisudtrlabk`tkrea rijel`.

    4. Dcllh glr XA,HA,IQT,Bd%--!@lrokc1. ART-^/K--!@lrokc8. OX--!@lrokc9. TDQ -!@lrokc7. Q. arikte`e`i-!`lrokc:. Dcllh urik-!`lrokc2. Q. akcaeuo -@lrokc5. Kcfkce`i pblspbktksi- @lrokc

  • 8/14/2019 Fibrous dysplasia: A case report on Treatment of Shapherd crooks deformity in Firous dysplasia -

    4/7

    8

    Lpirktel` `lti

    Xbrlujb cktirkc kpprlkab uppir i`h lg tbi giour wksixplsih. Lutir pkrt lg tbi prlxeokc giour wks sl tbe` tbkt et

    `iihs cettci igglrt tl auritti tbi aystea kriks akriguccy. Kgtiraurittkji vucjus wihji lstiltloy wks hl`i ktsudtrlabk`tkrea rijel` tl alrriat higlroety, okssevi errkhektihkccljrkgt wetb geduckr kutljrkgt wks kppceih tl i`bk`ai bikce`jk`h e`alrplrktel` lg tbi aystea dl`y cisel` k`h grkjoi`ts wirigexih wetb prlxeokc giolrkc `kec (^G@). Zlu`h wks aclsih e`ckyirs dy fiipe`j k hrke` e`sehi wbeab wks riolvih kgtir82blurs. Qteabis wiri riolvih kgtir ;>tbplst lpirktevi hky k`htbi bikce`j wks sktesgkatlry. Kdhuatel` dkr wks kppceih kgtiralopcitel` lg tbi lpirktel` tl prltiat tbi wikfi`ih dl`i glr 4ol`tbs. Kgtir riolvkc lg tbi kdhuatel` dkr kt 4 ol`tbsace`eakccy k`h rkhelcljeakccy dl`i wks stkdci k`h u`ete`jsktesgkatlrecy. Bi wks khvesih tl usi arutab glr `l` wiejbtdikre`j lg bes rejbt clwir ceod uptl 1 ol`tbs.

    Bestlpktblcljeakc riplrt

    Aurittih oktirekc wks si`t glr betlpktblcljeakc stuhy k`hriplrt sblws gedrlus hyspcksek.

  • 8/14/2019 Fibrous dysplasia: A case report on Treatment of Shapherd crooks deformity in Firous dysplasia -

    5/7

    9

    ^ri-lpirktevi Tkhelcljeakc ^eaturi

    ^ck`i R-rky Tt. Yppir giour (^rilpirktevi)

  • 8/14/2019 Fibrous dysplasia: A case report on Treatment of Shapherd crooks deformity in Firous dysplasia -

    6/7

    7

    ^lst Lpirktevi rkheljrkpb.

    ^lst lpirktevi pirelh wetb hirltktel` DkrGlcclw-up veset

  • 8/14/2019 Fibrous dysplasia: A case report on Treatment of Shapherd crooks deformity in Firous dysplasia -

    7/7

    :

    Hesaussel`

    Gedrlus hyspcksek es k hiviclpoi`tkc heslrhir e` wbeab

    trkdiauckr dl`i kri ripckaih dy aiccuckr gedrlus tessui kggiatstbi se`jci dl`i (ol`lstktea) lr ok`y dl`is (plcystktea). Qokccse`jci cisel`s kri ksyoptloktea. Ckrji ol`lstktea cisel`akusis pke` & oky hiviclp pktblcljeakc grkaturis. Xbi delpsyoky riqueri glr istkdcesbe`j hekj`lses. Qloi cisel`s okyrislcvis spl`tk`iluscy & viry ckrji higlroih aystea cisel`swetb pktblcljeakc grkaturi riqueri spiaekc surjeakc oiksuri glralrriatel` lg higlroety, gexktel` lg dl`i dy `kece`j,stri`jtbi`e`j lg dl`i dy dl`i jrkgte`j. K oexturi lg alrteakc &ak`aicclus dl`i oky prlvehi khhih stri`jtb ivi` tbes cisel`

    es `lt guccy irkheaktih. E` tbes u`usukc higlroih aksi wiakriguccy pck``ih tl auritti tbi aystea kriks lg dl`i, cktirkc

    wihje`j glr alrriatel` lg tbi vkrus higlroety, prlxeokc giolrkc`kece`j wks hl`i glr oke`tke`e`j rihuatel` & stkdecety, k`hirrkhektih ak`aicclus dl`i oexih wetb geduckr alrteakc dl`iwiri e`trlhuaih e` tbi cisel` tl i`bk`ai e`alrplrktel`,stri`jtbi`e`j & u`el` lg tbi dl`i. Xbes es k rkri & heggeauctaksi tl trikt. Kgtir kppcye`j tbes prlaihuri e` QbkbiihQurbkwkrhy Oiheakc alcciji Blspetkc, u`el` wks kabeivih e`

    usukc teoi, dl`i jrkgt wks `eaicy e`alrplrktih & okxeouohiglroety bks dii` alrriatih & sblrti`e`j wks kcsl lviraloiglcclwe`j lpirktel`.

    Tigiri`ai

    ;. Kpciys Qystio lg Lrtblpkiheas k`h grkaturis.2tbihetel` .4>>; . ;:8-;:9

    4. Akopdiccs Lpirktevi Lrtblpkiheas. ;>tbihetel`. 4>>1. :581.Xurifs Lrtblpkiheas, ^re`aepci & tbier kppceaktel`. 9tbihetel`. ;558.

    455-1>>.8. Khkos M.A. Lutce`i lg Lrtblpkihea. ;4tbihetel`, Aburabecc Ceve`jstl`.

    ;559. 91-98