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Osteogenesis imperfecta (compression fractures)
OI-blue sclera
Osteopetrosis(Albers-Schonberg)-osteoclast defect, Inc. bone mass but still brittle
Osteochondromatosis
Risk for malignancy?
Chondrosarcoma
Osteochondromatosis
Osteochondromatosis
Osteochondromatosis
Osteochondromatosis w/ cartilage cap
TB in the spine (eponym)? Pott’s Dz
TB-granulomas, giant cells
Calcium stain-Normal Bone
Ca stain-Osteoporosis (Loss of Bone density)
Thick skull? Paget’sHearing loss, Inc. serum Alk Phos, Inc. urine hydroxyproline
Sxs?
At Risk?
osteosarcoma,
CHF
Fibrous dysplasia of the rib
Polyostotic FD + Café au Lait & Early Puberty?McCune-Albright
Fibrous Dysplasia-too much stroma
Osteoid osteoma
Osteoid osteoma
Osteoblastoma
Osteosarcoma-Codman’s Triangle #1 primary mal bone
Osteosarcoma-kids with Rb at risk, Chr 13 del
Adults with previous radiation or Paget’s
Osteosarcoma
Telangiotic type
Osteosarcoma-Telangiotic type
Osteosarcoma-appendicular bones
Chondroma
Oiler’s-multi (one side
Of the body)
Mafucci’s-multi & hemangioma
Chondroma
Chondrosarcoma-axial bones
Chondrosarcoma-#2 primary mal bone
Chondrosarcoma
Chondrosarcoma-single mitosis is Dx
Ewing’s sarcoma-t(11,22)
(PAS+ ) Ewing’s
Liposarcoma-cell type?
Flouret cell (multinucleated lipoblast)
Liposarcoma type? Well-diff/low grade
Liposarcoma type? Myxoid most common t12,16
Liposarcoma-myxoid signet ring cells
Liposarcoma-Pleomorphic w/ Giant lipoblast
Liposarcoma-Round cell
Liposarcoma-ugly looking isn’t it?
Mal Fibrous Histiocytoma-#1 soft tissue mal
Mal Fibrous Histiocytoma-giant cells
Mal Fibrous Histiocytoma
Mal Fibrous Histiocytoma
Synovial Sarcoma-biphasic epitheloid and spindle cell
Synovial Sarcoma-biphasic epitheloid and spindle cell
Synovial Sarcoma-not synovial tissue
Synovial Sarcoma