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• DEVIATIONS OF NORMAL EVOKE SUSPICION
• OTHER ORGAN SYSTEM SHOULD BE EVALUATED TO RULE OUT OTHER GENETIC AND CHROMOSOMAL DISORDERS
DEVELOPMENTAL DYSPLASIA OF THE HIP
• CONGENITAL DYSPLASIA OF THE HIP
• CONGENITAL DISLOCATION OF THE HIP
• CONGENITAL SUBLUXATION OF THE HIP
• LIGAMENTOUS LAXITY IS DETECTABLE AT BIRTH
• NEONATES ARE ASYMPTOMATIC
• LIMP, WADDLING GAIT PATTERN, OR A LIMB LENGTH DISCREPANCY
• BARLOW TEST
• ORTOLANI MANEUVER
• GALEAZZI SIGN
COXA VARA
• DECREASE IN THE NORMAL NECK-SHAFT ANGLE OF THE FEMUR
• ASSOCIATED WITH CONGENITAL SHORT FEMURAL PROXIMAL FOCAL DEFICIENCY
• ABDUCTOR MUSCLE WEAKNESS, TRENDELENBURG GAIT ABNORMALITY, LIMB LENGTH DISCREPANCY
CONGENITAL DISLOCATION OF THE KNEE
• HYPEREXTENSION OF THE KNEE AT BIRTH
• ASSOCIATED ABNORMALITIES SUCH AS HIP DISLOCATION OR CLUBFOOT
CONENITAL DISLOCATON OF THE PATELA
• MAY NOT APPARENT FOR SEVERAL MONTHS AFTER BIRTH
• PERSISTENT FLEXION CONTRACTURE OF THE KNEE AND EXTERNAL ROTATION OF THE LEG
• THE PATELLA MAY NOT BE PALPABLE IN ITS DISLOCATED LATERAL POSITION
ANTEROLATERAL BOWING OF THE TIBIA
• MIGHT OR MIGHT NOT APPARENT AT BIRTH
• OFTEN ASSOCIATED WITH NEUROFIBROMATOSIS
• PROGRESSES TO CONGENITAL PSEUDOARTHROSIS OF THE TIBIA
CALCANEOVALGUS FOOT
• MARKED DORSOFLEXION OF THE ANKLE
• DEFICIENT ACTIVITY OF THE PLANTAR FLEXORS
• LIPOMYELOMENINGOCELE OR SOME OTHER NEUROLOGIC CONDITION
CONGENITAL VERTICAL TALUS
• RIGID FLATFOOT DEFORMITY
• IDIOPATHIC, FAMILIAL, OR ASSOCIATED WITH NEUROMUSCULAR OR CHROMOSOMAL ABNORMALITIES
CONENITAL SHORT FIRST METATARSAL
• SHORTHENING AND OFTEN ASSOCIATED WITH HALLUX VARUS
• PROBLEM WITH SHOE WEAR
POLYDACTYLY
• THE PRESENT OF ACCESSORY TOE
CLUBFOOT
• CONGENITAL TALIPES EQUINOVARUS (CTEV)
• PLANTAR FLEXION(EQUINUS)OF THE ANKLE, ADDUCTION(VARUS) OF THE HEEL, HIGH ARCH(CAVUS) AT THE MID FOOT, AND ADDUCTION OF THE FOREFOOT
• DD/ NEUROMUSCULAR CLUBFOOT, ARTHROGRYPOSIS, CONGENITAL CONSTRICTION SYNDROME
SYNDACTYLY
• THE LACK OF NORMAL SEPARATION BETWEEN FINGERS OR TOES
• VARY FROM WEB OF SKIN TO A BONY FUSHION (SYNOSTOSIS)
• GROWTH MAY CAUSE PROGRESSIVE DEVIATION OF THE CONJOINED FINGERS
CONGENITAL RADIO-ULNAR SYNOSTOSIS
• THE PROXIMAL ENDS OF THE RADIUS AND ULNA FAIL TO SEPARATE
• INABILITY TO PRONATE AND SUPINATE THE FOREARM
CONGENITAL DISLOCATION OF THE RADIAL HEAD
• MOST COMMONLY DEVELOPS POSTERIORLY AND TYPICALLY BILATERAL
• ELBOW DEFORMITY AND LIMITED MOTION
• THE DISLOCATED RADIAL HEAD OFTEN PRESENT AND PALPABLE PROMINENCE ON THE LATERAL SIDE OF THE ELBOW
• LIMB LENGTH DISCREPANCY INCREASES AS THE CHILD GROWS
• PATIENT CAN BE QUITE FUNGTIONAL WITH A POSTHESIS
PROXIMAL FEMORAL FOCAL DEFICIENCY
• DYSGENESIS OF THE PROXIMAL FEMUR WITH COXA VARA AND/OR PSEUDOARTHROSIS OF THE FEMORAL NECK
• SHORTENING OF THE FEMUR IS MARKED
HYPOPLASIA/ABSENCE OF THE THUMB
• HYPOPLASTIC THUMB MAY BE SMALL, OR THIN DUE TO DEFICIENT DEVELOPMENT OF THE THENAR MUSCULATURE
TRANSVERSE DEFICIENCY OF THE FOREARM
• CONGENITAL BELLOW ELBOW AMPUTATION
• CONGENITAL CONSTRICTION BAND SYNDROME