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CHAPTER 214 GLYCOGEN STORAGE DISEASES 1354 214 GLYCOGEN STORAGE DISEASES JOSEPH I. WOLFSDORF AND DAVID A. WEINSTEIN DEFINITION Glycogen, a highly branched polymer of glucose, is the storage form of glucose in mammals. e major sites of glycogen deposition are skeletal muscle and liver. Several other tissues and organs, including cardiac and

Goldman's Cecil Medicine Volume 665 || Glycogen Storage Diseases

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Page 1: Goldman's Cecil Medicine Volume 665 || Glycogen Storage Diseases

CHAPTER  214  GLYCOGEN STORAGE DISEASES1354

214 GLYCOGEN STORAGE DISEASESJOSEPH I. WOLFSDORF AND DAVID A. WEINSTEIN

DEFINITIONGlycogen, a highly branched polymer of glucose, is the storage form of glucose in mammals. The major sites of glycogen deposition are skeletal muscle and liver. Several other tissues and organs, including cardiac and