FIBROUS DYSPLASIA: CASE PRESENTATION- At Shaheed Suhrawardy Medical College Hospital, Dhaka, Bangladesh

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  • 8/9/2019 FIBROUS DYSPLASIA: CASE PRESENTATION- At Shaheed Suhrawardy Medical College Hospital, Dhaka, Bangladesh.

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    NyLr. Al @jzruc OscjaANNX, A.sh. (Nod-ablohjc B`eo`bbro`e).

    J hjsb ^bpdrt

  • 8/9/2019 FIBROUS DYSPLASIA: CASE PRESENTATION- At Shaheed Suhrawardy Medical College Hospital, Dhaka, Bangladesh.

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    Vjrtohucjrs dg tmb

    pjtob`t

    @jab9 ^jnouc Oscja

    Jeb9 >6 ybjrs

    Eb`lbr9 Ajcb

    Jllrbss9 Gucnjroj, Nderj

    Dhhupjtod`9 Cjndur

    Ajrotjc stjtus9 Ajrrobl

    ^bcoeod`9 Auscoa

    Ljtb dg jlaossod`9:5.6?.6?

    Ljtb dg bxjao`jtod`9:5.6?.6?

  • 8/9/2019 FIBROUS DYSPLASIA: CASE PRESENTATION- At Shaheed Suhrawardy Medical College Hospital, Dhaka, Bangladesh.

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    Hmobg hdapcjo`ts

    Vjo` & lbgdraoty jt tmb roemt uppbr tmoem gdr 5ad`tms gdccdwo e j trjuaj.

    Erjlujc smdrtb`o`e dg tmb roemt cdwbr coan wotm

    loggohucty o` wjcko`e gdr 7 ad`tms.

  • 8/9/2019 FIBROUS DYSPLASIA: CASE PRESENTATION- At Shaheed Suhrawardy Medical College Hospital, Dhaka, Bangladesh.

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    Mostdry dg prbsb`t

    occ`bss

    Jhhdrlo`e td tmb stjtbab`t dg tmb pjtob`t, mb wjs

    rbjsd`jncy wbcc 5 ad`tms njhk, tmb` sullb`cy mb gbctldw` d` tmb erdu`l ny jhholb`tjc trjuaj.

    Mb hducl wjck gdccdwo`e trjuaj wotmdut suppdrt, jgtbr

    wmohm mb `dtohbl aocl, goxbl jhmo`e pjo` o` tmb roemt

    uppbr tmoem wmohm wjs `dt jssdhojtbl wotm gbvbr,`d`-rjlojto`e & jeerjvjtbl luro`e wjcko`e &

    o`hdapcbtbcy rbcovbl ny tjko`e sdab pjo` koccbrs.

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  • 8/9/2019 FIBROUS DYSPLASIA: CASE PRESENTATION- At Shaheed Suhrawardy Medical College Hospital, Dhaka, Bangladesh.

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    Mostdry dg pjst occ`bss

    Mb mjl `d mostdry dg tunbrhucdsos.

    Mb os `d` Lojnbtoh

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    Gjaocy mostdry

    @d`b dg mos gjaocy abanbr suggbrbl

    grda suhm occ`bss.

    Vbrsd`jc mostdry

    Mb os `dt sadkbr

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    Xdhod-bhd`daoh

    Cdwbr aollcb hcjss gjaocy

    Oaau`ozjtod` mostdry

    Oaau`ozbl jejo`st tunbrhucdsos

    & tbtj`us

    Lrue mostdry

    M/D tjko`e @XJOLs td rbcobvb pjo`

  • 8/9/2019 FIBROUS DYSPLASIA: CASE PRESENTATION- At Shaheed Suhrawardy Medical College Hospital, Dhaka, Bangladesh.

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    Eb`brjc bxjao`jtod`

    Jppbjrj`hb9 Occ cddko`e

    Ndly nuoct9 Jvbrjeb

    Hd-dpbrjtod`9 Hd-dpbrrjtovb

    Lbhunotus9 D` hmdohb

    J`jbaoj9 Jnsb`t

    Iju`lohb9 Jnsb`t

    Hyj`dsos9 Jnsb`t

    Dblbaj 9 Jnsb`t

    \bapbrjturb9 `drajc

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    Eb`brjc bxjao`jtod`..hd`t.

    Vucsb9 57 nts/ao`

    Ncddl prbssurb9 ::6/56 aa dg Me

    ^bsporjtdry rjtb9 :7 /ao` Lbmylrjtod`9 @d soe`

    Kdocd`yhmoj9 Jnsb`t

    Cbukd`yhmoj9 Jnsb`t

    Hcunno`e9 Jnsb`t

    @bhk vbo`9 @dt b`edrebl IWV9 @dt rjosbl

    Cyapm `dlbs9 @dt pjcpjncb

    \myrdol ecj`l9 @dt pjcpjncb

    Xko` poeab`tjtod`9 Jnsb`t

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    Cdhjc bxjao`jtod`9 (^oemt Rppbr

    tmoem)Cddk9

    J` occ lbgo`bl lbgdraoty dhhupyo`e jt tmbsupbrd-cjtbrjc jspbht dg tmb uppbr roemt tmoemwotm hd`vbxoty j`tbrd-cjtbrjccy.

    Xko` dvbr tmb lbgdrabl jrbj os `drajc

    Wjrus lbgdraoty dg mop wotm smdrtb`o`e dg tmbcdwbr coan.

    R`jncb td wjck wotmdut suppdrt.

    Ujsto`e dg tmb tmoem, & ecutbjc aushcbs

    @d b`edrebl vbo`.

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    Cdhjc bxjao`jtod`9 (^oemt Rppbr tmoem)

    Gbbc9\mbrb os j` orrbeucjr, bxpj`lbl nd`y lbgdraotywotm hd`vbxoty j`tbrd-cjtbrjccy bxtb`lo`e grdatmb mop td suntrdhmj`tbroh jrbj. cdhjctbapbrjturb `drajc, aocl tb`lbr`bss prbsb`t,

    dvbr cyo`e sko` os grbb.Xmdrtb`o`e dg coan - ? ha.

    Aushcb wjsto`e-

    Ecutbjc - < ha.

    \moem< ha.Cbe8 ha

    Lostjc `burdvjshucjr stjtus `drajc

    ^beod`jc cyapm `dlbs `dt b`cjrebl.

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    Cdhjc bxjao`jtod`9 (^oemt Rppbr tmoem)

    Advbab`t9

    wjck wotm suppdrt.

    \rb`lbcb` Nures tbst pdsotovb ^oemt Mop (^DA)

    Gcbxod` 6-:666 [`drajc 6-:>66Q

    Bxtb`sod` 6-26 [`drajc 6->66Q

    Jnluhtod` 6-26 [`drajc 6-26Q

    O`tbr`jc rdtjtod` jt ?6

    6

    gcbxod` 6->6

    6

    [6-

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    Xystbaoh bxjao`jtod`9

    Cdhdadtdr systba

    Ejot9Hj` wjck wotm suppdrt

    O`spbhtod`9Wjrus lbgdraoty - roemt mop

    Vjcpjtod`9\b`lbr`bssjggbhtbl jrbj

    Xpo`b9 @drajc

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    @brvdus systba bxjao`jtod`

    Moembr psyhmoh gu`htod`9 @drajc

    Hrj`ojc `brvb bxjao`jtod`9 @drajc

    Adtdr gu`htod`9

    O`spbhtod`9Erdss Aushcb wjsto`e o` roemtmop, tmoem & cbe

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    Vjcpjtod`9Nuck dg aushcb9Ujsto`e Mop-

  • 8/9/2019 FIBROUS DYSPLASIA: CASE PRESENTATION- At Shaheed Suhrawardy Medical College Hospital, Dhaka, Bangladesh.

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    @brvdus systba

    bxjao`jtod`hd`t.

    Vdwbr9 [A^H shjcbQ

    Mop (rt.)9

    bxtb`sdr- > o`tbr`jc rdtjtdr- 6 ybjrs dcl aj`, hdao`e

    grda Gucnjroj, Njeurj jlaottbl o` Xmjmbbl

    Xumrjwjrly Ablohjc Hdccbeb Mdspotjc wotm tmb

    hdapcjo`ts dg pjo` & lbgdraoty jt tmb rt. Rppbr

    tmoem gdccdwo`e j aocl jhholb`tjc trjuaj 5 ad`tms

    njhk & erjlujc smdrtb`o`e dg rt. Cdwbr coan wotm

    loggohucty o` wjcko`e gdr 7 ad`tms.

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    Xjcob`t gbjturb.hd`t.

    \mb pjo` wjs aocl , goxbl, `d` rjlojto`e, jhmo`e o``jturb wmohm wjs `dt jssdhojtbl wotm gbvbr,

    jeerjvjtbl luro`e wjcko`e & o`hdapcbtbcy rbcovbl

    ny tjko`e @XJOLs.

    Mb jcsd `dtohbl j nb`lo`e lbgdraoty o` supbrd-cjtbrjc jspbht dg roemt tmoem wmohm wjs erjlujccy

    o`hrbjso`e o` sozb hjuso`e smdrtb`o`e dg tmb

    jggbhtbl coan

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    Xjcob`t gbjturb.hd`t.

    Dtmbr pjrts dg tmb ndly wbrb `drajc wotm `d

    mostdry dg wboemt cdss dr j`drbxoj. `d`b dg mosgjaocy abanbr suggbrbl grda suhm occ`bss.

    D` eb`brjc bxjao`jtod`, tmb pjtob`t os occ-

    cddko`e, `dt j`jbaoh, `d` ohtbroh, `dradtmbraoh,

    `dradtb`sovb & sko` poeab`tjtod` os jnsb`t.

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    Xjcob`t gbjturb.hd`t.

    D` cdhjc bxjao`jtod`, j` occ lbgo`bl, aoclcy pjo`gucndwo`e lbgdraoty wjs sbb` dhhupyo`e jt tmb supbrd-

    cjtbrjc jspbht dg tmb roemt tmoem wotm hd`vbxoty j`tbrd-

    cjtbrjccy bxtb`lo`e grda tmb mop td suntrdhmj`tbroh

    jrbj wotm Hdxj Wjrj. Dvbrcyo`e sko` & cdhjctbapbrjturb wjs `drajc.

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    Xjcob`t gbjturb.hd`t.

    Xmdrtb`o`e dg tmb coan wjs gdu`l ? ha tmj` tmb cbgt.

    Mb wjs u`jncb td wjck wotmdut suppdrt.

    \mbrb wjs erdss aushcb wjsto`e o` rt. Cdwbr coan,

    abjsuro`e ecutbjc- < ha, tmoem-

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    Xjcob`t gbjturb.hd`t.

    Lostjc `burdvjshucjr stjtus wjs `drajc &

    ^beod`jc cyapm `dlbs wbrb `dt b`cjrebl.\rb`lbcb` Nurestbst wjs pdsotovb wotm rbluhbl

    ^j`eb dg advbab`t (^DA) o` mop o` jcc

    lorbhtod`. ^DA dg k`bb & j`kcb wjs `drajc.

    \mb spo`b wjs `drajc. Dtmbr systbaohbxjao`jtod` rbvbjcs `d jn`drajcoty.

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    Loggbrb`tojc loje`dsos

    Eoj`t hbcc tuadr

    B`hmd`lrdajJ`burysajc Nd`b Hyst

    Nrdw` tuadr

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    O`vbstoejtod`s

    :. ]-^jy roemt tmoem wotm mop J/V & cjtbrjc vobw9

    Xmdws Xmbpmjrls hrddk lbgdraoty (`bhk-smjgtj`ecb9 ?66) wotm auctopcb dstbdcytoh cbsod`s

    o`vdcvo`e pjrt dg tmb `bhk, trdhmj`tbroh &

    suntrdhmj`tbroh jrbj, wotm tmo``o`e dg hdrtohjc

    nd`b & cuhb`t pjthmbs typohjccy mjzy, cddks cokberdu`l-ecjss jppbjrj`hb wotm pjtmdcdeohjc

    grjhturb jt tmb suntrdhmj`tbroh rbeod`.

  • 8/9/2019 FIBROUS DYSPLASIA: CASE PRESENTATION- At Shaheed Suhrawardy Medical College Hospital, Dhaka, Bangladesh.

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    Goe9 ]-^jy roemt tmoem wotm mop J/V & cjtbrjc

    vobw

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    O`vbstoejtod`s

    Ncddl gdr

    \H dg UNH ?,666 / hu aa

    LH dg UNH

    @ 27% N 6%

    C>7% A 2%

    B ea / lc

    Rro`b ^AB

    @drajc stuly H]^-V/J vobw@drajc Hmbst skojerja

    A\@dt soe`ogohj`t

    ^NX 57 aea / lc

  • 8/9/2019 FIBROUS DYSPLASIA: CASE PRESENTATION- At Shaheed Suhrawardy Medical College Hospital, Dhaka, Bangladesh.

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    O`vbstoejtod`s

    X. hrbjto`o`b6.? aea/ lc

    Ncddl urbj86 aea / lc

    X. hjchoua? aea / lc

    X. jckjco`b pmdspmjtbs::6 OR/ C

    G@JH @d ajcoe`j`t hbcc gdu`l,

    d`cy hbccucjr gonrdus tossub prbsb`t.

  • 8/9/2019 FIBROUS DYSPLASIA: CASE PRESENTATION- At Shaheed Suhrawardy Medical College Hospital, Dhaka, Bangladesh.

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    Ad`dstdtoh gonrdus lyspcjsojwotm XmbpmjrlsHrddk

    lbgdraoty o` uppbr b`l dg roemtgbaur wotm pjtmdcdeohjc

    grjhturb

    Hd`gorajtdry loje`dsos

  • 8/9/2019 FIBROUS DYSPLASIA: CASE PRESENTATION- At Shaheed Suhrawardy Medical College Hospital, Dhaka, Bangladesh.

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    \rbjtab`t

    \mos pjtob`t wjs u`lbr ed`b gdr sureohjc

    trbjtab`t d` :5-:6-6?

    Vrdhblurb9

    \mrduem cjtbrjc jpprdjhm uppbr b`l dg tmb gbaur wjs

    bxpdsbl Dutbr pjrt dg tmb prdxoajc gbaur wjs sd tmo` tmjt ot

    `bbls cottcb bggdrt td hurjtb tmb hystoh jrbjs hjrbguccy.

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    \rbjtab`t.hd`t.

    Vrdhblurbhd`t.9

    Jgtbr hurbttjeb vjceus wbleb dstbdtday wjsld`b jt suntrdhmj`tbroh rbeod` td hdrrbhtlbgdraoty, ajssovb orrjlojtbl jccderjgt wotmgonucjr jutd erjgt wjs jppcobl td b`mj`hbmbjco`e & o`hdrpdrjtod` dg tmb hystoh nd`y

    cbsod` & grjeab`ts wbrb goxbl wotm prdxoajcgbadrjc o`tbrcdhko`e `joc (VG@).

  • 8/9/2019 FIBROUS DYSPLASIA: CASE PRESENTATION- At Shaheed Suhrawardy Medical College Hospital, Dhaka, Bangladesh.

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    \rbjtab`t.hd`t.

    Vrdhblurbhd`t.9 Udu`l wjs hcdsbl o` cjybrs ny kbbpo`e j lrjo`

    o`solb, wmohm wjs rbadvbl jgtbr

  • 8/9/2019 FIBROUS DYSPLASIA: CASE PRESENTATION- At Shaheed Suhrawardy Medical College Hospital, Dhaka, Bangladesh.

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    Mostdp-jtmdcdeohjc ^bpdrt

    Xmdws cddsb hbccucjr gonrdustossub wotm wolb sprbjl pjthmbs dg

    oaajturb nd`b - Xueebstovb dg

    Gonrdus lyspcjsoj.

  • 8/9/2019 FIBROUS DYSPLASIA: CASE PRESENTATION- At Shaheed Suhrawardy Medical College Hospital, Dhaka, Bangladesh.

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    Goe9 Vdst dpbrjtovb pbrodl

  • 8/9/2019 FIBROUS DYSPLASIA: CASE PRESENTATION- At Shaheed Suhrawardy Medical College Hospital, Dhaka, Bangladesh.

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    Goe9 Vrbdpbrjtovb ]-rjy `d :5.6?.6?

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    Goe9 Vdst dpbrjtovb ]-rjy ^t. Rppbr Gbaur

    D` :6tmVDL Jgtbr 5 wbbks

  • 8/9/2019 FIBROUS DYSPLASIA: CASE PRESENTATION- At Shaheed Suhrawardy Medical College Hospital, Dhaka, Bangladesh.

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    Goe9 Vdst dpbrjtovb ]-rjy ^t. Rppbr Gbaur

    Jgtbr 8 ad`tmsJgtbr < ad`tms