HD-12: Female Genital Development

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Female Genital Development

• Normal development• Duplication• Agenesis• UG Sinus• Imperforate hymen• CAH

Dr. Richard Schlussel, M.D., Assistant ProfessorDepartment of Urology, Columbia University

HD-12: Female Genital Development

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Hypospadias Hypospadias repair

Hypospadias repair

• Paramesonephric duct– A.K.A. Mullerian Duct– Becomes future

• Fallopian tubes• Uterus• Upper 2/3 vagina

VAGINAL AND UTERINEDUPLICATION

HD-12: Female Genital Development

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Bicornuate Uterus

Didelphys uterus

Unicornuate UterusComplete Vaginal Duplication

• Symptom– Blood persists despite

tampon duringmenses

• Symptom– Upper vagina fills

with blood duringmenses

HD-12: Female Genital Development

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Mayer-Rokitansky-Küster-Hauser Syndrome

1 in 5,000births

VAGINALAGENSIS

Normal Hymenal Ring

Imperforate hymen

Mucous due to maternalhormones

HD-12: Female Genital Development

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Intra-op drainage of imperf hymenUROGENITAL SINUS

UROGENITAL SINUS

X X

CONGENITAL ADRENAL HYPERPLASIA (CAH)

CAH 46 XX

HD-12: Female Genital Development

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• Association withUrinary TractAnomalies– Renal agenesis– Ectopic ureters