Embed Size (px)
Citation preview
Duke Cameron, MDDivision of Cardiac SurgeryDivision of Cardiac Surgery
No financial disclosures
No disclosures
No financial disclosures
Acknowledgement of Drs.Vricella, Black and Dietz
2
Loeys-Dietz Syndrome
3
LDS Aortopathy
• Root Aneurysm• Root Aneurysm
• Arterial Tortuosity
• Dissection/Rupture at• Dissection/Rupture atyoung age and smallaortic sizeaortic size
• Peripheral aneurysms• Peripheral aneurysms
4
Aortic Root Replacement in LDS
5 79 LDS operations
Operative Experience with LDS
6
ARR in LDS: Operative Technique
7
Bentall Reimplantation VSRR
8
Concomitant Procedures
9
Operative Results
10
11
Late Results
12
No reoperations for AR in trileaflet David VSRRs
Special Considerations
•
•
•
13
Coronary artery button aneurysms
“Hershey Kiss” aneurysms
Arch Reinterventions in LDS
Mos
15
LVOT Pseudoaneurysm
• Typically arising from subanular• Typically arising from subanularsutures in NC sinus, thru aorto-mitral apron
• Can be PSA or fistula to LA or• Can be PSA or fistula to LA orRA
16
Conclusions: ARR in LDS
• Low operative risk (0% mortality)
• Valve sparing operations have good• Valve sparing operations have goodearly and midterm results
• High re-intervention rate• High re-intervention rate
• Close surveillance necessary postop• Close surveillance necessary postop
17
Recommendations
18
