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Khairan Irmansyah Departement Of Otolaryngology MEDICAL SCHOOL OF PADJADJARAN UNIVERSITY BANDUNG 2010 01/22/2010 1 kh-lr

Cleft PalateKH LR

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Cleft Palate

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  • Khairan IrmansyahDepartement Of Otolaryngology

    MEDICAL SCHOOL OF PADJADJARAN UNIVERSITY

    BANDUNG

    2010

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  • Incidence And Epidemiology Greater in female (3/4)The incidence of submucous CP is 1 per 1600 birthsThe incidence of bivid uvula is 1 per 800 live births

    Cleft Palate :Schism in the roof of the oral cavity.01/22/2010*kh-lr

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  • EtiologyStrongly dependent on genetic factorsClefting is heterogenous and result also from enviromental insultsEnviromental Factors:- Fetal alcohol exposure- cigarette smoking- folic acid deficiency or antagonist- phenytoin- retinoic acid derivatives

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  • Amniotic band syndromeMaternal diabetes4. Multivitamins with folic acid likely reduce the incidence of clefting

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  • Anatomy & Physiology The palate is the scaffold for midface structures. Consists : Hard palate (anterior) Soft palate (posterior) 01/22/2010*kh-lr

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  • Hard PalateIncisive foramen (delimits the anterior)Premaxilla(centrally)Draped the prepalatal structures, alveolus, lip, nasal floor, alar cartilages

    Soft palateBony maxillaeContigous palatine bonesLateral pterygoid laminaeInterposed hamulus

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  • Skeletal Anatomy01/22/2010*kh-lr

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  • Muscle & Skeletal Anatomy01/22/2010*kh-lr

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  • MuscleTensor veli palatiniBroadFlatNearly vertical paired musculotendinous structuresArises from the major wing of the sphenoidal spine superiorly and posteriorly and from the anterolateral part of the eustachian tube Function: - Stabilizing the velum at the level of the hamulus- dilating the eustachian tube in concert with the tensor tympani- with tensor palatini retracting the eardrum and increasing tubal pressure01/22/2010*kh-lr

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  • Levator veli palatiniCylindrical paired musclesPosterior bundles arises from the base of skull & the external carotid foramenForm a sling to swing the velum backward & upwardParticipate in swallowing and speech

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  • Passavants bar: Midline posterior portion of pharyngeal sphincter, which may become thickened during sphincter contraction to facilitate closure

    Velopharyngeal mechanism swallowing & passing air (during speaking, whistling, or blowing) innervated by the vagus & glossopharyngeus (for swallowing), and the facial nerve (for speech)01/22/2010*kh-lr

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  • Hence four major muscles arches or sling exist:The levatorSuperior constrictorPalatopharyngeusPalatoglossus

    Palatopharyngeal sphincter of Willis:During active constraction the two loops of the superior pharyngeal constrictor and levator form a sphincteric closure of theVelopharyngeal space and jointly01/22/2010*kh-lr

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  • Greater Palatine foramen:a greater palatine arterya greater palatine nervus01/22/2010*kh-lr

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  • Innervation Anatomy01/22/2010*kh-lr

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  • Blood Suply Anatomy 01/22/2010*kh-lr

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  • ClasificationBivid uvulaIncomplete cleft of secondary palateUnilat. Complete CL & CPBilat. Complete CL & CP01/22/2010*kh-lr

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  • SpeechNormaly consonans build up of nasal pressureCleft patients produce speech marked by :HypernasalityNasal air emissionsWeak pressure consonants or plosivesCompensatory articulation

    The earliest age at which formal speech therapy is ussualy innitiated as approximately 4 years01/22/2010*kh-lr

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  • Clinical EvaluationHealt history :- family history of clefting- history of illness or maternal ingestion of medication during the 1st trimester- other deformities to incriminate a particular syndrome (ex. Pierre Robin or KlippelFeil)Physical examination: - the defect is associated with a cleft lip or not- whether the cleft is complete or incompleteand unilateral or bilateral01/22/2010*kh-lr

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  • - Determine whether there are associated:1. 1st branchial arch or nasal deformities2. Narrowing of the interocular distance3. Extensive defect- Examine the tympanic membranes for serous otitis, hypernasality01/22/2010*kh-lr

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  • CLEFT PALATE REPAIRPreoperative Diagnostic MeasuresGeneral examinationClinical findingsRadiographic examination Lateral teleradiographs

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  • Indications and Timing of SurgerySpeech patologists end of the first year of lifeOrthodonthists recommendWith the development of atraumatic cleft palate surgery, a consensus has emerged in favor of an early repairA single-stage palate repair 12-15 mounth of age

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  • Two-stage palate repair:a. Anterior to posterior (AP) sequence : Total cleft, the hard palate repaired at 9-12 months, soft palate at 12-15 monthsb. Posterior to anterior (PA) sequence :Prymary veloplasty 6 monthsCleft hard palate after eruption of the prymary dentition

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  • Cleft Palate Repair01/22/2010*kh-lr

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  • Preoperative PreparationsPosition :-Supine with the neck slightly hyperextended01/22/2010*kh-lr

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  • Special Instrument01/22/2010*kh-lr

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  • Operation Technique01/22/2010*kh-lr

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  • The Schwenkendiek two stage repair closes the sof palate cleft and leaves the hard palate cleft for obturation with a prothesis until delayed closure at 4 to 5 years. Minimal disturbance of facial growth. Requires frequent changes of prothesis. Result in significant speech disorder if not properly obturated. Management SURGICAL REPAIRPalatoplasty technique01/22/2010*kh-lr

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  • Von Langenbacecks palatoplasty advances bipedicle mucopeiosteal flaps : Easy to perform,Decreased denuded palatal bone, Does not provide increased palatal lengthManagement SURGICAL REPAIRPalatoplasty technique01/22/2010*kh-lr

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  • V-Y Push Back Palatoplasty retrodisplaces two posteriorly based mucoperiosteal flaps by a V to Y closure techq: Lengthens the palate, Leaves a large, raw palatal surface Management SURGICAL REPAIRPalatoplasty technique01/22/2010*kh-lr

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  • Two Flap Palatoplasty (Bardach) utilizes two posterioly placed mucoperiosteal flap that extend to the alveolar cleft. Good for complete cleft of palatal/alveolusManagement SURGICAL REPAIRPalatoplasty technique01/22/2010*kh-lr

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  • The Furlow Palatoplasty utilizes a double reversing Z plasty of musculomucosa and mucosa only flaps to repair the palatal cleft. Usually used for submucosal or soft palate cleft. Good speech results with proper muscle aligment. Dificult for wide cleftSURGICAL REPAIRPalatoplasty technique01/22/2010*kh-lr

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  • Operative TechniquePedicle flaps01/22/2010*kh-lr

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  • V-Y advancement01/22/2010*kh-lr

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  • Management SURGICAL REPAIRUnilateral Cleft Palate 01/22/2010*kh-lr

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  • Management SURGICAL REPAIRUnilateral Cleft Palate Repair01/22/2010*kh-lr

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  • Management SURGICAL REPAIRUnilateral Cleft Palate Repair01/22/2010*kh-lr

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  • Management SURGICAL REPAIRBilateral Cleft Palate Repair01/22/2010*kh-lr

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  • Management SURGICAL REPAIRCleft Palate Repair01/22/2010*kh-lr

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  • Reference Points and PitfallsA few landmarks are important in cleft palate repair: The incisive foramen The posterior nasal spine The greater palatine foramen The hamulus and the fascia of the medial pterygoid muscle01/22/2010*kh-lr

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  • Several potential hazards should be noted: Bleeding from the palatine artery Post operative bleeding Tearing of the nasal layer during its dissection behind the hard palate Tearing of the vomerine flap during its dissection at the neck of the premaxilla Necrosis at the anterior tip of a long palate flap

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  • If the soft palate is drawn againts the pharyngeal wall by a suction tube passed into a nostril at the end of the operation while the nostril are held shut, this is considered proof that the length and function of the velum are satisfactory01/22/2010*kh-lr

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  • Postoperative Care Palatal tissue are apposed to the underlying bone by pledget held in place with sutures.Nasogastric tubeProphylactic antibioticsPatient out of bed on the 1st op.dayPacking is remove after 5 days

    The sutures are removed from the palatal mucosa on day 12Exercises puffing and blowing (in small children)Systematic speech therapy (4 years of age)

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  • Complications Hemorrhage respiratory obstruction Suture line dehiscence Fistula

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  • Highlights Cleft lip and palate occurs in 1 in 1,000 births; cleft palate alone occurs in 1 in 2,000 births. Cleft palate and lip is the most common congenital malformation involving the head and neck, and a cleft palate team approach best provides long term multidiscipliary management. Cleft palate repair is ussually performed at 9 to 12 months of ages as long as the child is gaining weight and growing in a normal fashion01/22/2010*kh-lr

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    *01/22/2010