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Assessment of Inherited Colour Vision Defects in Clinical Practice Yasmine; Maram; Kholoud; Rami 30/03/2013 1

Assessment of Inherited Colour Vision Defects

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Page 1: Assessment of Inherited Colour Vision Defects

Assessment of Inherited Colour

Vision Defects in Clinical Practice

Yasmine; Maram; Kholoud; Rami 30/03/2013

1

Page 2: Assessment of Inherited Colour Vision Defects

contents

The purpose of the discussion

Introduction to CVD.

Diagnostic tests for CVD.

Management

Advices to patients

Special Occupations and CVD

Short glossary

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Maram Hajir

Page 3: Assessment of Inherited Colour Vision Defects

Purposes

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To recommend tests for primary care assessment of colour vision

To Learn you about the methods and analysis for tests

To give you an info. About Management for CVD

To provide guidance on the advice that can be given to patients with

CVD

Maram Hajir

Page 4: Assessment of Inherited Colour Vision Defects

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The retina of the human eye contains about 7

million cone cells

and more than 100 million rod cells that enable

normal vision.

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Color is light, which is carried as specific

wavelengths that the eye absorbs and the brain

converts into messages so that we ‘see colors.

Page 6: Assessment of Inherited Colour Vision Defects

Colour Vision Deficiency ( CVD )

Colour vision deficiency (CVD) is the

inability to distinguish certain shades of color or in

more severe cases, see colours at all.

It is a common functional disorder of vision.

Prevalence of CVD among Caucasian population is

reported as 8% on males and 0.4% on females

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Maram Hajir

Page 7: Assessment of Inherited Colour Vision Defects

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The mood of inheritance

Maram Hajir

Page 8: Assessment of Inherited Colour Vision Defects

Classifications of CVD

-Typical Monochromasy( rare)

-Blue cone Monochromasy ( rare)

-Protanopia (1% of men 0.01% women)

-Deuteranopia (1% of men 0.01% women)

-Tritanopia (1 in 13,000 both men & women equally)

-Protanomaly (1% of men 0.03% women)

-Deuteranomaly (5% of men 0.35% women)

-Tritanomaly (rare)

Monochromasy

Dichromasy

Anomalous

trichromasy

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Maram Hajir

Page 9: Assessment of Inherited Colour Vision Defects

Monochromasy T

yp

ical

Mon

och

rom

asy

(ra

re)

mechanism

mutation of genes encoding the cone-specific alpha

and beta sub-units of the cation channel

Characteristics

Colour blind. No perception of colours. Colours

distinguished by brightness differences only. Very

insensitive to red light.

Nystagmus.

Low visual acuity 6/36 to 6/60

Painless photophobia.

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Maram Hajir

Page 10: Assessment of Inherited Colour Vision Defects

Cont.

Blu

e co

ne

mo

no

chro

ma

sy mechanism

S (blue) cone pigment only.

Characteristics

Colour blind. Colours distinguished by brightness

differences only.

Rudimentary colour vision in mesopic vision from rod

and blue cone activation.

Very insensitive to red light.

Nystagmus.

Low visual acuity 6/12 to 6/24.

Painless photophobia.

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Maram Hajir

Page 11: Assessment of Inherited Colour Vision Defects

Dichromasy

Pro

tan

op

ia (

1%

of

men

0.0

1%

wom

en)

mechanism

Absence of L (red) cone pigment.

Characteristics

Very reduced ability to identify colours.

Confuse red, yellow and green, white and green, and

blue and purple.

Reduced sensitivity to red light.

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Maram Hajir

Page 12: Assessment of Inherited Colour Vision Defects

Cont.

Deu

teran

op

ia (

1%

of

men

0.0

1%

wom

en)

Mechanism

Absence of M (green) cone pigment.

Characteristics

Very reduced ability to identify colours.

Confuse red, yellow and green, and white and green.

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Maram Hajir

Page 13: Assessment of Inherited Colour Vision Defects

Cont.

Tri

tan

op

ia (

1 i

n 1

3,0

00 b

oth

me

&

wom

en e

qu

all

y)

mechanism

Absence of S (blue) cone pigment.

Characteristics

Very reduced ability to identify colours.

Confuse blue with blue green and green, and white

with yellow.

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Maram Hajir

Page 14: Assessment of Inherited Colour Vision Defects

Anomalous trichromasy

P

rota

nom

aly

(1%

of

men

0.0

3%

wom

en)

mechanism

L (Red) cone pigment absorption spectrum shifted to

shorter wavelengths of light

Characteristics

May confuse white with green and confuse reds,

yellows and greens but loss of colour discrimination

varies greatly between individuals.

Reduced sensitivity to red light.

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Maram Hajir

Page 15: Assessment of Inherited Colour Vision Defects

Cont.

Deu

teran

om

aly

(5%

of

men

0.3

5%

wom

en)

mechanism

M (Green) cone pigment absorption spectrum shifted

to longer wavelengths of light.

Characteristics

May confuse white with green and confuse reds,

yellows and greens but loss of colour discrimination

varies greatly between individuals.

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Maram Hajir

Page 16: Assessment of Inherited Colour Vision Defects

Cont.

Tri

tan

om

aly

(ra

re)

mechanism

Partial loss of S cone pigment.

Characteristics

Loss of colour discrimination for blues, blue-greens,

and greens.

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Maram Hajir

Page 17: Assessment of Inherited Colour Vision Defects

Tests that used in CVD detection

CVD

Jasmine R. AbdulRahman 30/03/2013

17

Page 18: Assessment of Inherited Colour Vision Defects

Types of tests

Ishihara test

Farnsworth Panel D‐15

Farnsworth‐ Munsell 100‐hue

Medmont C100 test

Richmond HRR test (2002)

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Jasmine R. AbdulRahman

Page 19: Assessment of Inherited Colour Vision Defects

Isochromatic Vs Pseudoisochromatic!

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Pseudoisochromatic plates frequently are used by

eye specialists to get an idea of one’s color

efficiency or deficiency. i.e.:

The Ishihara color test

Richmond HRR 2002

SPP2

Dvorine

Jasmine R. AbdulRahman

Page 20: Assessment of Inherited Colour Vision Defects

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Jasmine R. AbdulRahman

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“isochromatic”: To a color-deficient person,

all the dots in one or more of the plates will appear

similar or the same.

“Pseudoisochromatic” : To a person without

a color deficiency, some of the dots will appear

dissimilar enough from the other dots to form a

distinct figure (number) on each of the plates

Jasmine R. AbdulRahman

Page 22: Assessment of Inherited Colour Vision Defects

Ishihara test

It was created by Dr. Shinobu

Ishihara (1879‐1963).

designed to detect congenital

color deficiencies.

Ishihara contains 38 plates.

Pseudoisochromatic plates

History Ishihara plates

http://www.guldenophthalmics.com/ccp7/media/ecom/prodl

g/Ishihara-Color-Test-Book.jpg

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Jasmine R. AbdulRahman

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Capability

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Detects protan and deutan CVD with high sensitivity

and specificity.

Jasmine R. AbdulRahman

Screening Congenital Acquired Ability to

classify

No. of plates

Yes Yes No No 38

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Methods

Dr. Liana, Please chose one paper from this box :D

Please read the name that you select.

Please …. If you don’t mind, the test will be done on

you.

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Jasmine R. AbdulRahman

Page 25: Assessment of Inherited Colour Vision Defects

Methods

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lit adequately by daylight or under electric light

Electric light should be as far as possible to resemble the effect of the natural

daylight

The plates are held 75 cm from the subject and tilted

the plane of the paper is at right angles to the line of vision

each answer should be given without more than three seconds delay.

If the subject is unable to read numerals, plates 26-38 are used and the

winding lines between the two X’s are traced with the brush. Each

tracing should be completed within ten seconds

Jasmine R. AbdulRahman

Page 26: Assessment of Inherited Colour Vision Defects

Methods

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In a large scale examination the test may be

simplified to an examination of six plates only 1. No 1

2. one of the Numbers 2, 3, 4, 5

3. one of Numbers 6, 7, 8, 9

4. one of Numbers 10,11, 12, 13

5. one of Numbers 14, 15, 16, 17

6. one of Numbers 18,19,20,21.

It may be necessary to vary the order of the plates if it is

suspected that there is a deliberate deception on the part

of the subject.

Jasmine R. AbdulRahman

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Word Document

Jasmine R. AbdulRahman

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Plate number How normal read How red-green Deficiencies read How total blind

read

No. 1 12 12 12

No. 2 8 3 X

No. 4 29 70 X

No. 6 5 2 X

No. 7 3 5 X

No. 8 15 17 X

No. 9 74 21 X

No.11 6 X or read incorrectly X

No. 13 45 X or read incorrectly X

No. 14 5 X or read incorrectly X

No. 15 7 X or read incorrectly X

No. 16 16 X or read incorrectly X

No. 17 73 X or read incorrectly X

No. 18 X 5 X

No. 20 X 45 X

Strong

protan

Mild Protan Strong

Deutan

Mild Deutan

No.22

26

6 2 & 6 (6 clearer) 2 2 & 6 (2 clearer)

No. 23 42 2 4 & 2 (2 clearer) 4 4 & 2 (4 clearer)

Page 29: Assessment of Inherited Colour Vision Defects

How to interpret results

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Scoring occurs on the first 21 plates

17/21 or more is considered normal

13/21 or less is abnormal.

Jasmine R. AbdulRahman

Page 30: Assessment of Inherited Colour Vision Defects

Interpretation

Errors on three or more of the numeral plates indicates red-

green CVD with a small chance (2%) of misdiagnosing

normal colour vision.

Five or more errors indicates certain red-green CVD.

Number of errors is not a useful measure of severity.

Subjects making very few errors will probably have a mild defect

but those who make a large number of errors may be mild or severe.

Failure to see the red numeral indicates protan.

failure to see the red-purple numeral indicates deutan.

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Jasmine R. AbdulRahman

Page 31: Assessment of Inherited Colour Vision Defects

Care of the book

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Book of the test plates should be kept closed.

Except during use :P

Exposure to sunlight causes a faiding of the color of

the plates.

Use sterile cotton swap in tracing plates.

Don’t touch the plate.

Jasmine R. AbdulRahman

Page 32: Assessment of Inherited Colour Vision Defects

Farnsworth Panel D‐15

designed by Dean

Farnsworth

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History Farnsworth Panel D‐15

http://www.e-mfp.org/Assets/Farnsworth_Panel1.jpg

Kholoud Abu Abdoun

Page 33: Assessment of Inherited Colour Vision Defects

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most widely used of the colour sorting tests and

must be part of primary care colour vision

assessment.

Kholoud Abo Abdoun

Screening Congenital Acquired Ability to

classify

No. of plates Time to

Administer

Yes Yes Yes Yes 16 chips Slow

Page 34: Assessment of Inherited Colour Vision Defects

Purposes

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To reveal the color blindness

To differentiate among subjects affected with

Dyschromatopsia ( little affected abnormal

trichromatic) from those who are

Severely affected ( dichromatic)

Kholoud Abo Abdoun

Page 35: Assessment of Inherited Colour Vision Defects

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Description of the test

Cautions It is recommended:

Not to expose the caps to light.

To avoid touching the colors with fingers.

To avoid damage the caps and their colors

Kholoud Abo Abdoun

Page 36: Assessment of Inherited Colour Vision Defects

Methods

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Either on Daylight or on front of a wide window and under a clear sky.

The position for examiner and patient is a cross the table.

The caps numbered from 1-15 are arranged in random order.

The subject educated to choose the cap after cap and arrange them on the case based on the color degree as he/she see.

patient start from the reference cap P.

Kholoud Abo Abdoun

Page 37: Assessment of Inherited Colour Vision Defects

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To eliminate the waste time, examiner told the patient that the test take only 1-2 minutes to finish.

anyway examiner let the patient to finish normally.

Those who finished quickly, ask him to check their classifications.

The case is closed and turned over; it is now ready for future testing.

Starting from the reference cap, the points of diagram are connected according to the order presented by the subject.

Kholoud Abo Abdoun

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PDF

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Kholoud Abo Abdoun

Page 41: Assessment of Inherited Colour Vision Defects

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Kholoud Abo Abdoun

Page 42: Assessment of Inherited Colour Vision Defects

Interpretation

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The results of the test can be either a:

”success” circular diagram.

or “failure” diagram with parallel lines

http://webvision.med.utah.edu/imageswv/KallColor25.jpg

Page 43: Assessment of Inherited Colour Vision Defects

The diagrams of subject

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Either normal or slightly deficient follow the circle.

For color blind subject the diagrams from parallel

or crisscrossed lines (with at least two parallel lines

crossing the diagram)

Note: test should be repeated in the event of a

doubtful interpretation.

Kholoud Abo Abdoun

Page 44: Assessment of Inherited Colour Vision Defects

some cases of success and failure

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Example of success: normal and slightly deficient results. The subjects with normal vision place the caps in a perfect order or in interchanging one or two caps .

Example of failure: results of color blind subjects.

Fig. 4 shows the diagram of a red blind patient (dichromatich). The lines f diagram are parallel to the protan axis.

Fig. 6 shows the diagram of a subject blind to blue or purple with lines parallel to the tritan axis.

There is a very uncommon case of complete color blindness: the patient will be totally unable to place the caps in a logical order.

Kholoud Abo Abdoun

Page 45: Assessment of Inherited Colour Vision Defects

Richmond HRR

The HRR pseudoisochromatic test was developed by Hardy, Rand and Rittler.and it is supports very efficient color defeciency screening

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History

Maram Hajir

Page 46: Assessment of Inherited Colour Vision Defects

Capability

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1. Detects protan and deutan CVD with a sensitivity

and specificity only slightly less than that of the

Ishihara test.

2. Ideal confirmation test for the Ishihara test.

3. Detects tritan defects

4. May differentiate protan, deutan and tritan

defects.

5. Classifies severity as mild, medium and strong.

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Maram Hajir

Page 48: Assessment of Inherited Colour Vision Defects

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It serves as a confirmation of the result of the

Ishihara test and can guard against the possibility

that the patient has learned the correct answers for

the Ishihara. It has a sensitivity and specificity

almost as good as the Ishihara. It can also detect

tritan defects, which the Ishihara does not.

Maram Hajir

Page 49: Assessment of Inherited Colour Vision Defects

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This might be thought to be of little importance as

inherited tritan defects are rare, having a prevalence

of only 1 in 13,00021 and blue and yellow are not

as important in colour codes as are red, green and

yellow, however, tritans can encounter occupational

colour problems.

Maram Hajir

Page 50: Assessment of Inherited Colour Vision Defects

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So do u think that HRR can detect the aquired CVD

?

Maram Hajir

Page 51: Assessment of Inherited Colour Vision Defects

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Yes , by popular configuration of the HRR , called

the HRR Combo and provides the full 24 plates

laminated with plastic to protect them against the

acid in fingerprints. The Combo also provides a full

set of Amsler Grids. Amsler testing completes the

prescribed regimen for acquired color testing

Maram Hajir

Page 52: Assessment of Inherited Colour Vision Defects

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The last advantage of the HRR test is that it can be

used with very young children because it uses

symbols, a circle, a triangle and a cross, which can

often be named or traced by young children before

they can read numbers.

Maram Hajir

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Alternatively, key cards can be made so children

can identify the symbols they see.

Maram Hajir

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Richmond HRR (24 plates )

first 4 plates to show how the test work

the fourth plate has no

figure

4 plates for R/G

screening

contain 6 symbols

2 plates for tritan

screening

contain 4 sbmbols

14 plate for extent

10 for R/G 4 for blue

CVD

Maram Hajir

Page 55: Assessment of Inherited Colour Vision Defects

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Two or more errors with the six symbols on the four red-green screening

plates indicates abnormal colour vision but a few patients (4%) with

normal colour vision will make two errors.

Three or more errors indicates certain red-green CVD. The majority (98%)

of those with a red/green defect make three or more errors on the screening

plates.

No data on detection of tritan defects with the Richmond HRR 2002 test

but the screening plates of the original AO HRR test have been shown to

detect tritan defects, but not all.

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If no errors are made on the four symbols on the two tritan screening plates ask if one of each pair of symbols in the tritan screening and classification plates is much fainter than the other. If the tritan symbols look fainter, a tritan defect is probable.

Correct classification as protan or deutan on 86% of occasions, 3% wrongly classified, remainder ambiguous. Tritan defects clearly differentiated if detected.

Errors in first five classification plates indicates mild CVD (30% CVDs). Errors on next three classification plates = medium CVD (45% CVDs) Errors on last two classification plates = strong CVD (25% CVDs). However, meaning of ‘medium’ and ‘severe’ is uncertain as some mild CVD are classified ‘medium’ or ‘strong’ and dichromats may be classified as ‘medium’.

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Maram Hajir

Page 58: Assessment of Inherited Colour Vision Defects

Medmont C100 test

The Medmont C-100 owes it origin to Estvez and colleagues.

who thought of applying the principle of flicker photometry to the assessment of colour vision.

The first commercially available instrument using this principle was the OSCAR, produced by a Dutch company Medilog

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History Medmont C100 test

http://www.medmont.com.au/medi

a/2722/c100_top.jpg

Jasmine R. AbdulRahman

Page 59: Assessment of Inherited Colour Vision Defects

Overview

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The Medmont C-100 test is not well known but it

must be a part of the basic battery of colour vision

tests.

It has only one function, which is to differentiate

protans and deutans among those who have red-

green abnormal colour vision

Jasmine R. AbdulRahman

Page 60: Assessment of Inherited Colour Vision Defects

Overview

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objective screening of colour anomalies and

reductions.

It is an inexpensive test and takes only a minute or

two to administer.

Jasmine R. AbdulRahman

Page 61: Assessment of Inherited Colour Vision Defects

Features

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1. Rapid colour deficiency indication

2. Unique, easy to read scale (graphic colour bar indicator)

3. Portable, with mains operated power pack (no batteries)

4. 3 Years Warranty

5. Comes with protective case, plug-in mains power pack and User Guide.

6. Dimensions (mm): 70W x 35H x 113L

Jasmine R. AbdulRahman

Page 62: Assessment of Inherited Colour Vision Defects

Procedure

1. Normal room light conditions are suitable but any fluorescent lights which exhibit noticeable flicker should be switched off.

2. The subject was asked to hold the instrument at a distance of about 40 cm, and look at the small circular flickering disk.

http://www.medmont.com.au/products/c100-colour-vision-tester.aspx

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Steps Medmont C100

Jasmine R. AbdulRahman

Page 64: Assessment of Inherited Colour Vision Defects

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Page 65: Assessment of Inherited Colour Vision Defects

Recommendations

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The experimenter records the readings as shown on

the indicator at the rear of the instrument.

It is recommended that the patient be given two

practice attempts at obtaining a minimum flicker

point, and the measurements should be repeated at

least four times for statistical averaging.

Jasmine R. AbdulRahman

Page 66: Assessment of Inherited Colour Vision Defects

Results Analysis

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The settings chosen to achieve no or minimum

flicker are read on an arbitrary scale from -5 to

+ 5.

+2.0 to -2.0 is the extreme range of normal

settings

but typically settings are within ± 1.0

The scale is colour-coded red for protan

settings, green for deutan and yellow for

normal

The colour-coded scale lights correspond to

integers (1, 2, 3 ...)

but can be interpolated to 0.5, when two

adjoining lights are illuminated.

Jasmine R. AbdulRahman

Page 67: Assessment of Inherited Colour Vision Defects

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If two adjacent LEDs are equally illuminated, the

reading would be halfway between the two LED

values.

if the two yellow LEDs are equally illuminated, the

reading would be zero.

Similarly, if a yellow LED and its adjacent green LED

are equally illuminated, the reading would be 1.5

Page 68: Assessment of Inherited Colour Vision Defects

Results

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The Medmont C-100 can also diagnose women

who have normal colour vision but are carriers of

the abnormal gene for protanomaly or protanopia.

The Medmont C-100 colour vision test measures

relative spectral sensitivity using flicker photometry

to differentiate protans and deutans. It should be able

to diagnose Schmidt's sign.

Jasmine R. AbdulRahman

Page 69: Assessment of Inherited Colour Vision Defects

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PDF

Page 70: Assessment of Inherited Colour Vision Defects

Fransworth‐ Munsell 100‐hue

designed by Dean

Farnsworth

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History

Rami Danaa

http://www.utsl.co.th/upload/product/Munsell%2

0Color%20FM%20100%20Hue%20Test.jpg

Page 71: Assessment of Inherited Colour Vision Defects

Fransworth‐ Munsell 100‐HUE

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P

urp

ose

Divide persons with normal CV into classes of superior, average

and low color discrimination

Determining the type and severity of CVD

Rami Danaa

Page 72: Assessment of Inherited Colour Vision Defects

Fransworth‐ Munsell 100‐HUE

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Components

Four wooden cases

Lighting

Administrator-to-patient Position

Scoring sheet

Rami Danaa

Page 73: Assessment of Inherited Colour Vision Defects

Procedure

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Rami Danaa

Page 74: Assessment of Inherited Colour Vision Defects

Procedure

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Rami Danaa

Page 75: Assessment of Inherited Colour Vision Defects

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PDF

Page 76: Assessment of Inherited Colour Vision Defects

Indications of Re-testing

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Rami Danaa

Page 77: Assessment of Inherited Colour Vision Defects

Interpretation

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• About 68% of the population wit normal CV has average color discrimination

• The pattern will be characterized by TEC ranges from 20 to 100

Average discrimination

• About 16% of the population wit normal CV has superior color discrimination

• The pattern will be characterized by TEC ranges from zero to 16

superior discrimination

• About 16% of the population wit normal CV has low color discrimination

• The pattern will be characterized by TEC more than 100

Low discrimination

Rami Danaa

Page 78: Assessment of Inherited Colour Vision Defects

Interpretation

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Rami Danaa

Page 79: Assessment of Inherited Colour Vision Defects

Interpretation

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• The mid point is located between 62 and 70 Protans

• The mid point is located between 56 and 61 Duetans

• The mid point is located between 46 to 52 Triatns

Rami Danaa

Page 80: Assessment of Inherited Colour Vision Defects

Interpretation

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Rami Danaa

Page 81: Assessment of Inherited Colour Vision Defects

Limitation

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The major limitation of the test is the long time

required to perform the test and to analyze the

results.

Rami Danaa

Page 82: Assessment of Inherited Colour Vision Defects

To avoid waste time see the video

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Video

Page 83: Assessment of Inherited Colour Vision Defects

Why color vision test is not always done in

routine clinical practice?

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1. there is no single test of colour vision that

provides the clinician with all the information

needed to advise patients.

2. proper assessment of abnormal colour vision

needs several tests, which takes time, and the

clinician has to decide which supplementary

colour vision tests should be used.

Rami Danaa

Page 84: Assessment of Inherited Colour Vision Defects

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3. there is no treatment for abnormal colour vision so

there may seem little point in diagnosing it.

4. the classification of CVDs is complex and may

not be easily remembered by practitioners who do

not routinely diagnose abnormal colour vision

with an anomaloscope.

Rami Danaa

Page 85: Assessment of Inherited Colour Vision Defects

Treatment, „Compensation‟ & Cure

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• Some CVD sufferers can be helped by color filters which act to increase the contrast and reportedly make it possible to distinguish colors close to the confusion lines

• Some people benefit from the use of an X-Chrom lens which is available as a contact lens. Again, these filters may serve to increase color contrast. Further, spectacles that reduce glare may also help congenital CVD sufferers.

‘THERAPEUTIC’ METHODS

• In 2009 the Departments of Ophthalmology at the University of Washington in Seattle, the University of Florida in Gainsville and the Medical College of Wisconsin in Milwaukee published the results of a research program aimed at correcting the red-green vision of squirrel monkeys with congenital (dichromatic) CVD using gene therapy. It was shown that after applying gene therapy the monkeys were able to distinguish between patterns of gray, green and red dots.

GENE THERAPY RESEARCH IN PRIMATES

Rami Danaa

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In the absence of the development of a cure for

congenital CVD, safety remains a key issue. Those

with a strong or medium level of congenital CVD

need to avoid activities where color confusion may

jeopardize others.

Rami Danaa

Page 87: Assessment of Inherited Colour Vision Defects

Advice to Patients

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The difficulties of giving advice

There is always great potential for misunderstanding

and misremembering.

It should not be assumed that the patient who learns of

his abnormal colour vision for the first time will

receive the news with interest or gratitude

Rami Danaa

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Steward and Cole report that of the 18 patients in their survey who were

previously unaware of their abnormal colour vision, half expressed

disbelief and denied they had any problem with colour and half were

accepting and acknowledged that on reflection they did have problems

with colour.

Pickford and Cobb found 44 per cent of a sample of 36 subjects diagnosed

to have CVD for the first time exhibited denial, which they define as ‘a

wide range of attitudes from plain disbelief in the tests to an unwillingness

to agree that the defect, if it does exist, would have any influence on their

daily life’. Only 22 per cent of the sample demonstrated a coping attitude,

that is, acceptance of the defect and an effort to adapt. The rest of the

sample exhibited some form of overcompensation about their defect

Rami Danaa

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Career advice

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Some occupations have a statutory colour vision requirement

but these vary between countries and between states within

countries and are often poorly defined and administered.

There are also several occupations, for which there is no

statutory colour vision requirement but for which abnormal

colour vision is a handicap.

it is not possible to provide a comprehensive list and full

details of all occupational colour vision standards

Kholoud Abo Abdoun

Page 90: Assessment of Inherited Colour Vision Defects

Occupational colour requirements broad

categories

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1. Normal colour vision

2. Defective colour vision that is sufficiently mild

to enable the colour task to be performed

Kholoud Abo Abdoun

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orm

al c

olo

ur

vis

ion

Normal colour vision is required for occupations that involve precise colour matching

Also for occupations for which it is deemed that recognition of signal lights and other colour codes is absolutely critical

to safety

Examples: deck officers and seamen, train drivers, air traffic controllers

(in Australia) and some occupations in the defence forces

All patients with CVD, however mild, can be told that it is very likely that these careers will not be open to them.

Kholoud Abo Abdoun

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efec

tive

colo

ur

vis

ion

that is sufficiently mild to enable the colour

task to be performed

The two most common occupational colour tasks that give rise to an occupational colour vision standard are the recognition of signal lights and surface colour codes

Lantern test for recognition of signal lights

Farnsworth D15 test for surface colour codes

Kholoud Abo Abdoun

Page 93: Assessment of Inherited Colour Vision Defects

Lantern

The present instrument was developed when the College and the Association of Optometrists jointly organised a competition to meet the need for a new lantern design for certain British Aviation & Marine colour vision tests. In 2002 the CAM prototype lantern designed by Prof. R. Fletcher won the competition.

The Fletcher CAM Lantern

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History

Kholoud Abo Abdoun

Page 94: Assessment of Inherited Colour Vision Defects

Overview

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Lanterns are valuable practical ways of detecting colour vision defects, having been used in clinical, aviation and marine assessments for many years.

Lantern tests can instil confidence perhaps lacking with other conventional tests.

The task of naming small coloured lights resembles practical signals & transport situations

This is valuable in Optometric and Ophthalmological practice for inherited and acquired colour vision defects.

Kholoud Abo Abdoun

Page 95: Assessment of Inherited Colour Vision Defects

Typical Uses

1. tests for aircraft pilots, mariners, railway drivers

and other occupations.

2. assessment of inherited anomalies of colour

perception (about 5 – 8 % of the male

population).

3. detection of visual changes sometimes caused by

diabetes, cataract, retinal degeneration, etc

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Kholoud Abo Abdoun

Page 96: Assessment of Inherited Colour Vision Defects

Methods

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Naming the colours, at 6 metres reflected in a standard mirror, is the essential task.

Aviation and Clinical tests These are presented in a quiet room with illumination between 80 and 200 lux.

Two manual knobs at the back control the Aperture sequence & the Colour sequence.

A shutter exposes the coloured lights for 2 seconds, & subjects should respond within 5 seconds.

Kholoud Abo Abdoun

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Kholoud Abo Abdoun

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How Can Color Deficiencies Limit

Humans?

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Jasmine R. AbdulRahman

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Careers

Bus Driver, Firefighters, Police Officers, Paint Makers,

Doctors, Chemists, Decorators, Computer Programmers

School

Affects Reading and Math Skills

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Traffic signs

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Jasmine R. AbdulRahman

Normal Deuteranopes protanopes

relying on brightness or location, rather than color, to identify objects or situations

can help.

For example, by learning the order of the three colored lights on a traffic signal and

knowing that if the lowermost light is illuminated, it means that the light is green

Page 102: Assessment of Inherited Colour Vision Defects

Telecommunications and electrical

cables.

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They will recognise the blue and white cables but will be uncertain about the red, orange, brown and green.

Normal Deuteranopes protanopes

Jasmine R. AbdulRahman

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Colour indicates how well meat is

cooked?

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lack of perception of red makes it hard for them to identify the uncooked piece of meat.

Normal Deuteranopes protanopes

Jasmine R. AbdulRahman

Page 104: Assessment of Inherited Colour Vision Defects

Colour indicates ripeness of fruit

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Nearly 30 per cent of people with abnormal colour vision

report they have trouble judging the ripeness of fruit.

Normal Deuteranopes protanopes

Jasmine R. AbdulRahman

Page 105: Assessment of Inherited Colour Vision Defects

diagnosis of illness!!

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Medical practitioners and optometrists who have abnormal colour vision

often report that they have trouble seeing redness of inflammation.

18% of those with abnormal colour vision report that they have difficulty

seeing skin rashes, sunburn and blushing.

Normal Deuteranopes protanopes

Jasmine R. AbdulRahman

Page 106: Assessment of Inherited Colour Vision Defects

Colour is often used to distinguish an object from

others that are similar

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This is especially the case in police work, where colour is often used to describe suspects, evidence and motor cars.

They will be able to identify the yellow car and the blue, white and silver cars but not the red and green cars. Note that the illuminated brake lights in the red car in the second row of parked cars are not evident in the dichromatic transformations.

Normal Deuteranopes protanopes

Jasmine R. AbdulRahman

Page 107: Assessment of Inherited Colour Vision Defects

Denotative use of colour

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Colour is often used as an identifier at school.

An instruction to colour a drawing in a certain colour can be

bewildering for the colour vision deficient school child

Parents should write the names of the colours on the pencils.

Normal Deuteranopes protanopes

Jasmine R. AbdulRahman

Page 108: Assessment of Inherited Colour Vision Defects

Colour in search

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Colour often marks out objects and facilitates

search for them.

Normal Deuteranopes protanopes

Jasmine R. AbdulRahman

Page 109: Assessment of Inherited Colour Vision Defects

Colour and search

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Colour coding in maps is used to code the class of feature.

to mark out and differentiate for example, blue for district

names and route numbers.

Jasmine R. AbdulRahman

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Short Glossary

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Maram Hajir

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Achromatism/Achromatopsia

Rare inability to distinguish colors. See also Monochromacy.

Cone

Light-sensitive retinal receptor cell that provides sharp visual acuity and color discrimination. See also Rod.

Deutan

Refers to a person who has deuteranopia, a type of dichromatism in which red and green are confused. Also deteranomaly, a type of anomalous trichromatism in which an abnormally high proportion of the green is needed when mixing red and green to produce yellow.

Dichromatism

Moderately severe color vision defect in which one of the three basic color mechanisms is absent or not functioning.

Maram Hajir

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Protan

Refers to a person who has protanopia, a type of dichromatism in which only two hues are seen. Also protanomaly, a type of anomalous trichromatism in which an abnormally high proportion of the red primary stimulus is needed when mixing red and green to produce yellow.

Dyschromatopsia

Any type or degree of defective color vision.

HRR

Hardy-Rand-Rittler pseudoisochromatic plate test of colored dots that appear as recognizable geometric shapes. Used for identifying color vision deficiencies.

Ishihara

Pseudoisochromatic plate test similar to the HRR test, but with certain limitations.

Maram Hajir

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Monochromacy/ Achromatism/Achromatopsia

Rare inability to distinguish colors

Munsell Scale

Standardized scale of colored materials having

variations in hue and saturation.

Tetartan

Refers to a person with tetartanopia or tetartanopsia,

theoretical conditions and terms for a type of blue-

yellow blindness in which there are two neutral points.

Maram Hajir

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Trichromatic Requiring the use of three color mixture primaries to match all

perceived hues. Anomalous trichromatic is a form of defective color vision in which three primary colors are also required for color matching, but the proportion of primaries in the mixturematches are significantly different from those required in normal trichromatism.

Tritan Refers to a person having tritanomaly or tritanopia. The former is

a rare type of defective color vision in which an abnormally large proportion of blue must be mixed with green to match a standard blue-green stimulus. Tritanopia is a form of dichromatism in which all colors can be matched by suitable mixtures of only a red primary and a green or blue primary.

Maram Hajir

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References

Michael N. Wiggins, MD. How we should really be doing and interpreting the Ishihara. Retrieved by

March 16,2013 from www.jomtonline.com/jomt/articles/volumes/5/2/HowWeIshihara.pdf

Alotaibi Z.A et.al. Assessment of the Medmont C100 test for colour vision screening of male Saudi

Arabians. S Afr Optom 2011 70(1) 14-20

Ross W Harris & Barry L Cole. Diagnosing protan heterozygosity using the Medmont C-100 colour

vision test. Clin Exp Optom 2005; 88: 4: 240–247

Cole B.L, Lian K.L & Lakkis C. The new Richmon HRR Pseudoisochromatic test for color vision is better

that ishihara test. Clin Exp Optom 2006; 89: 2: 73–80

Maciej Laskowski. USING CUSTOMIZED PSEUDOISOCHROMATIC PLATES FOR

DETECTING CHOSEN FORMS OF DICHROMACY. Journal of KONES Powertrain and Transport,

Vol. 19, No. 1 2012

SHINOBU ISHIHARA. Ishihara Instructions. Retrieved by March 16,2013 from

white.stanford.edu/newlm/.../Ishihara.14.Plate.Instructions.pdf

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