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7/25/2019 4 Early Diagnosis in Neonatal Surgical Cases.pptx
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Early Diagnosis inNeonatal and Pediatric
Surgical Cases
Amir ThayebBatam 11 September 2015
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Kasus
60% kasus Bedah anak
kelainan
kongenital
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Early Diagnosis in Fetaland Neonatal Surgical
Cases
Amir ThayebBatam 11 September 2015
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Congenital anomaly (!"#
$enition &
' Strutural anomalies
' )untional anomalies
' *etaboli disorders
+hih are present at the timeo, birth-
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.elompok $eteksi $ini
1- /emeriksaanAntenatal
"bstetri
2- /emeriksaan Post natal
a-/ediatri bidan pera+at
b-Bedah Anak
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Antenatal Obstetri
S kelainan anatomis
3on 4nasie /renatal Testing 34/T
/emeriksaan darah 4bu .elainanmetabolik kromosom
Chorio entesis (plaenta#
Amnio entesis
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Antenatal Obstetri
.epustakaan &
S Tr $igestius &
' Atresias mg 12 17
' astroshisis 12 mg
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Antenatal Obstetri
.epustakaan &
S Tr $igestius &
' Atresias mg 12 17
' astroshisis 12 mg
/erlu ingat &
$inding perut menutup siologis mg 12 819
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Antenatal Obstetri USG
.epustakaan &
Tr $igestius & Atresias mg 12 17
astroshisis 12 mg
/erlu ingat &
kembalinya usus ke
intraabdominal mg 12819
:bh diperaya pemeriksaan ; 19
mg
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Incidence kepustakaan
Anorektal 1&5000
' *orbus !irshsprung 1& 5000
' "bstruksi $uodenum 1& 2500 ' sus halus 1&1500
' .elainan dinding perut 1&2000
' Atresia
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!KK!N
Setiap hari lahir 10 000bayi
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Incidence kepustakaan
Anorektal 1&5000
' *orbus !irshsprung 1& 5000
' "bstruksi $uodenum 1& 2500 ' sus halus 1&1500
' .elainan dinding perut 1&2000
' Atresia
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Kasus "S Cipto # $%&'
1- Atresia unum ? 4leum 217- "bstruksi @eto8Sigmoid (*! 52#
5- "bstruksi Anorektal 9
6- !ernia $ia,ragmatika 5
- .elainan $inding /erut 22
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&( Atresia Eso)agusAntenatal USG abdo*en
Cairan amnion; 2000 ml
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&( Atresia Eso)agusAntenatal USG le+er
S leher 2mg &
-Blind endmaDimal dilatation o,
esophagealpouh
pper pouhsi n
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&( Atresia Eso)agus , Postnatal
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&( Atresia Eso)agus , testNG-
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&( Atresia Eso)agus)oto kontras udara
.ontras
dara
.ontras
lain
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&( Atresia Eso)agus)oto kontras udara
.ontras
dara
.ontras
lain
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&( Atresia Eso)agus)oto kontras udara
.ontras
dara
T4$A.
/
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-ipe tersering
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-ipe tersering
Atresia
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-ipe tersering , A.asi
@egurgitasi asamlambung
Aspirasisalia
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Posisi persiapan
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$( Obstruksi Duodenu*Antenatal / double bubble
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Perbandingan ukuran gaster
Atresia
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$( Obstruksi Duodenu*Post natal , Klinis
*untah hi>au
' Abdomen tdk distensi ?hanya epigastrium
'
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$( Obstruksi Duodenu*Post natal / Double bubble
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$( Obstruksi Duodenu*Post natal / Double bubble
$$?
1- Atresia $uodenum
2- eb $uodenum
9- /anreas Annulare
7- *alrotasi
S? 3T dekompresi
@ehidrasi
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$( Obstruksi Duodenu*Post natal / Double bubble
S?
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$( Obstruksi Duodenu*Post natal / Double bubble
S?
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0( Obstruksi 1e2unu* 3Ileu*
*ultiple loop
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0( Obstruksi 1e2unu* 3Ileu*
Trias obstruksi &
8 *untah
8 $istensi Abdomen
8 $e,ekasi
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0( Obstruksi 1e2unu* 3Ileu*
Trias obstruksi &
8 *untah
8 $istensi Abdomen
8 $e,ekasi
S?
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'( Obstruksi "ecto/Sig*oid 34irsc+sprung
*ultipleloops-ambaran
sama dengan
Atresia 4leumdistal
atau
"bstruksiAnorektal
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'( Obstruksi "ecto/Sig*oid 34irsc+sprung
Gona
transisi
tdk
terlihatantenatal
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'( Obstruksi "ecto/Sig*oid 34irsc+sprung
.linis &
am
$istensi abdomen
"bstruksi @ekto Sigmoid &
olok dubur eakuasi,eses dan udara
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'( Obstruksi "ecto/Sig*oid 34irsc+sprung
$iagnosis &
1- am
2- .ontras enema usia 289
mg
9- Biopsi hisap
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5( Obstruksi anorektalAtresia ani
*ultipleloops-
ambaranAbdomensama dengan&
8 Atresia
4leum 8 *!
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5( Obstruksi AnorektalAtresia ani
Anus
@ektum
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Ano*ali ano/rektal
Tentukan &
Tinggi?rendah
)istula? tanpa
stula
:okasi stula
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Atresia Ani
)oto .neeChest
Tanpa stula
*inimal usia1 >m
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Atresia Ani
.olostomi
sia 2 mg kontrast pouh
/SA
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Cloaca Persisten
S 2 mg
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Cloaca Persisten
AnteriorCloaa
/osisirethra
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Cloaca Persisten
AnteriorCloaa
/osteriorCloaa
/osisirethra
/osisianus
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CloaaAnterior
Cloaa/osterior
/osisi rethra normal
/osisi Anusnormal
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)istulaHestibuler
Cloaa
rethraHagina )istel Hestibulum
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/erineumCloaa
/erineum dan Anusnormal
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Cloaca Persisten
$iagnosis &
' enitogram
' Cystosopy
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6( 4ernia Dia)rag*atika
=antung
asterintra
thoraD
Antenatal
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6( 4ernia Dia)rag*atika
elembungudara ? ususintra thoraD *inim bayangan
udara intra
.:434S
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6( 4ernia Dia)rag*atika
.linis
dyspnoe
bising na,as lemah
abdomen saphoid
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6( 4ernia Dia)rag*atika
Tindakan
8 Stabilisasi ? suporti,
8 Turunkan hipertensi
pulmonal!)" 3"
7 K l i di di t
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7( Kelainan dinding perutO*)alokel
$' 2a* 8&9$5:
7 K l i di di t
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7( Kelainan dinding perutO*)alokel &6 *g
$' 2a* 8&9$5:
)etus
"m,alokel
7 K l i di di t
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7( Kelainan dinding perutO*)alokel
Hisus
mbilikus Selaput amnion
7 K l i di di t
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7( Kelainan dinding perutGastrosc+isis
7 K l i di di t
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7( Kelainan dinding perutGastrosc+isis &6 *g
:oop usus halusdi ronggaamnion
7 K l i di di t
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7( Kelainan dinding perutGastrosc+isis &6 *g
-:oopusus
halus
-Tak ada
membran
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7( Kelainan dinding perut
"m,alokel peahastroshisis
/erlu segera di tutup
Bahaya !ipotermi
Siapkan 2 km operasi
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7( Kelainan dinding perut
@esusitasi&
8 @a+at dalam inkubator
8 Balut isus dengan kassa
8 3T untuk dekompresi
8 airan maintenane
8 persiapan operasi
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Ker2a sa*a yang erat
1- $iagnosis sebelum lahir
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-eri*a Kasi+